Table 1 Non-criteria manifestations among primary APS patients
Total number = 43 | Autoimmune cytopenia | APS nephropathy | Libman-Sachs endocarditis | Neurological non-criteria | Livedo reticularis |
|---|---|---|---|---|---|
Number | 17 (39.5) | 4 (9.3) | 5 (11.6) | 12 (27.9) | 8 (18.6) |
Type, n | ITP = 13 AIHA = 1 Evan’s syndrome = 3 | - | - | Multiple sclerosis-like disease = 4 Migraine = 6 Lymphocytic recurrent meningitides = 1 Seizures = 1 | - |
Associated non-criteria manifestations | APS nephropathy Livedo reticularis | ITP Livedo reticularis | Migraine Livedo reticularis | Libman-Sachs endocarditis | ITP APS nephropathy Libman-Sachs endocarditis |
Thrombotic phenotype (pure), n (%) | 10 (58.8) | 2 (50.0) | 2 (40.0) | 9 (75.0) | 4 (50.0) |
Obstetrical phenotype (pure), n (%) | 3 (17.6) | 0 ( 0.0) | 0 (0.0) | 3 (25.0) | 0 (0.0) |
Combined APS, n (%) | 4 (23.5) | 2 ( 50.0) | 3 (60.0) | 0 (0.0) | 4 (50.0) |
Triple positivity, n (%) | 10 (58.8) | 4 (100.0) | 3 (60.0) | 3 (25.0) | 4 (57.1) |
Relapse, n/total n (%) | 10/12 (83.3) | 4/4 (100.0) | 1/5 (20.0) | 3/10 (30.0) | 4/5 (80.0) |