Table 1 Clinical and laboratory characteristics of 17 patients with eosinophilic fasciitis
Sex/age of onset, y | Disease duration, mo | Clinical presentations | Laboratory examinations | Concomitant disorder | ||||||||||
|---|---|---|---|---|---|---|---|---|---|---|---|---|---|---|
Skin thickening | Arthralgia | Limited joint motility | Bilateral/Symmetrical | Myalgia | Eo% | Rheumatology | ESR (mm/h) | CRP (mg/l) | CK (U/L) | EMG | ||||
P1 | M/45 | 6 | Calf | Interphalangeal, knee | Knee, ankle | Y/Y | + | / | - | NL | NL | / | NL | - |
P2 | M/26 | 2 | Forearm, calf | Interphalangeal | Interphalangeal | Y/Y | + | 15.5% | / | 54 | / | 80 | NL | - |
P3 | M/22 | 4 | Forearm, calf | Elbow, wrist, ankle, knee, | Interphalangeal, ankle, knee | Y/Y | + | / | / | 38 | / | 54 | Myogenic | - |
P4 | M/59 | 1 | Forearm, calf | Interphalangeal, wrist, ankle | - | N/N* | + | 22.4% | ANA, p-ANCA | 110 | 53 | / | Neurogenic# | CSS |
P5 | M/59 | 1 | Forearm | Interphalangeal, ankle | Interphalangeal, ankle | Y/Y | - | NL | - | 24 | 14 | 33 | NL | - |
P6 | M/26 | 2 | Forearm | Interphalangeal, wrist | Interphalangeal, wrist | N/N* | + | / | ANA | NL | NL | 76 | NL | - |
P7 | F/63 | 6 | Forearm, calf | - | - | Y/Y | + | 9.6% | ANA | NL | NL | 36 | NL | Thrombocytopenia |
P8 | M/37 | 36 | Forearm, calf | Interphalangeal, wrist, ankle, knee | Interphalangeal, ankle | Y/Y | + | NL | ANA, RF | NL | NL | 42 | NL | - |
P9 | M/37 | 12 | Calf | - | - | N/N** | + | NL | / | 20 | NL | 94 | NL | - |
P10 | M/27 | 4 | Forearm, calf | Interphalangeal, wrist, ankle | Interphalangeal, wrist, ankle | Y/Y | - | 22.3% | ANA | 27 | 46 | 27 | NL | − |
P11 | F/16 | 4 | Forearm | Interphalangeal, wrist | Interphalangeal, wrist | Y/Y | - | 11.9% | - | NL | NL | / | NL | - |
P12 | M/37 | 24 | Forearm, calf | Interphalangeal, wrist | Interphalangeal, wrist | Y/Y | + | NL | ANA | 21 | 43.6 | 305 | NL | Papillary thyroid cancer |
P13 | M/61 | 12 | Forearm, calf | - | Interphalangeal, wrist | Y/Y | + | 15.5% | ANA | NL | 11.1 | 28 | NL | - |
P14 | F/20 | 24 | Forearm, foot | Interphalangeal, wrist, toe | Interphalangeal, wrist, toe | Y/Y | + | / | - | / | / | 42 | Myogenic | - |
P15 | M/69 | 6 | Forearm, calf | - | - | Y/Y | - | NL | - | 23 | 9.2 | 22 | NL | - |
P16 | F/40 | 2 | Forearm | - | Interphalangeal, wrist | Y/Y | + | NL | ANA, RF | 34 | 10.8 | / | Myogenic | - |
P17 | F/16 | 36 | Calf | - | - | N/N* | + | NL | Ha | 87 | / | 38 | NL | - |