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Table 2 Muscle pathological features of 16 patients with eosinophilic fasciitis

From: Clinicopathological profile of eosinophilic fasciitis: a retrospective cohort study from a neuromuscular disorder center in China

 

PFA

Necrotic fibers

Fasciitis

Perivascular

inflammation

Eosinophils

infiltration

CD3

CD8

CD4

CD68

MHC-I

MHC-II

MxA

MAC

P1

+

-

+

+

+

2

2

2

2

Diffuse

Focal + PF

-

-

P2

-

-

+

+

+

2

2

2

2

PF

PF

-

-

P3

+

+

+

+

-

2

2

2

2

PF

PF

-

Cap + Sarco

P4

+

-

+

+

-

2

2

2

2

-

-

-

-

P5

-

-

+

+

-

2

2

2

2

PF

PF

-

-

P6

-

-

+

+

-

2

1

2

2

PF

PF

-

-

P7

-

-

+

+

-

2

2

1

2

PF

PF

-

-

P8

-

-

+

+

-

2

2

1

2

PF

-

-

-

P9

-

-

+

+

-

1

1

1

2

Diffuse

-

-

-

P10

-

+

+

+

+

2

2

2

2

Diffuse

Focal + PF

-

Sarco

P12

-

-

+

+

-

2

1

2

2

Diffuse

Focal + PF

-

-

P13

+

-

+

+

-

2

2

2

2

Diffuse + PF

Diffuse +PF

-

Sarco

P14

-

-

+

-

-

1

1

1

2

PF

-

-

-

P15

-

-

+

+

-

2

2

2

2

Diffuse

Focal

-

-

P16

-

-

NA

-

-

0

0

0

1

PF

-

-

-

P17

-

-

+

+

-

2

2

1

2

Focal

-

-

-

  1. Abbreviations: PFA = perifascicular atrophy; NA = not available; MHC = major histocompatibility complex; MxA = myxovirus resistance protein; MAC = membrane attack complex; PF = perifascicular; Cap = capillary deposition; Sarco = sarcolemma deposition